Fructose bisphosphatase deficiency
CARBOHYDRATE METABOLIC DISORDER THAT HAS MATERIAL BASIS IN A DEFICIENCY OF FRUCTOSE-1,6-BISPHOSPHATASE RESULTING IN HYPOGLYCEMIA AND METABOLIC ACIDOSIS ON FASTING DUE TO INSUFFICIENT FRUCTOSE BISPHOSPHATASE FOR GLUCONEOGENESIS
Fructose-1,6-diphosphatase deficiency
In fructose bisphosphatase deficiency, there is not enough fructose bisphosphatase for gluconeogenesis to occur correctly. Glycolysis (the breakdown of glucose) will still work, as it does not use this enzyme.